Non-ketotic hyperglycemic hemichorea (NHH) also known as diabetic striatopathy or chorea, hyperglycemia, basal ganglia (C-H-BG) syndrome, is a rare cause of unilateral basal ganglia hyperdensity. The patients glucose was 20 when checked.

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Loeys-Dietz syndrome is an autosomal dominant connective tissue disorder that has many similar features to Marfan syndrome causing toruosity of vessels of the neck, in this case both vertebral arteries and the internal carotid arteries.

T1 weighted images demonstrate multiple foci of similar signal intensity to grey matter. Findings are in keeping with Subependymal Nodular Heterotopia in this patients causing seizures.